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The Korean Journal of Pathology 2007;41(5): 334-336.
Diffuse Ganglioneuromatosis of Appendix associated with Von Recklinghausen;s Disease.
Young Su Kim, Sang Chul Nam, Man Hoon Han, Jeong Shik Kim, Ji Yun Jeong, Han Ik Bae
Department of Pathology, Kyungpook National University School of Medicine, Daegu, Korea. baehi@knu.ac.kr
Gastrointestinal ganglioneuromatosis is a rare neoplastic condition that can occur in association with von Recklinghausen's disease with multiple endocrine neoplasia type II B. The main locations are the ileum, colon, and appendix. We report a case of diffuse ganglioneuromatosis of the appendix associated with a mesenteric and ileocecal plexiform neurofibroma in von Recklinghausen's disease.
Key Words: Ganglioneuromatosis; Appendix; Von Recklinghausen's disease