Acardius is more uncommon situation that occur in a pair of monozygotic twin. Abnormal fetuses of this variety are never found in single pregnancies, and circulation of blood is only by virtue of communication with the vessels supplying the normal twin. Acardia shows various other defects in addition to the absence of heart. The most common form is the acardius acephalus, they are headless and lack thoracic organs and upper extremities. The abdominal organs might contain remnants of liver, spleen, kidney, or intestine. Underdeveloped gonads are occasionally found. Recently authers experienced a acadius acephalus in 28 year-old female and herein reported with literature review.