Abstract

A case of von Willebrand's disease of a 10-year-old girl is presented with the brief review of literature. The patient was admitted to the Department of Pediatrics, Seoul National University Hospital with the chief complaint of frequent epistaxis. She had normal platelet count, prolonged bleeding time, prolonged aPTT, 4% of platelet adhesiveness, 30% of factor VIII procoagulant activity, 39% of factor VIII related antigen, less than 1.6% of ristocetin cofactor, and normal ristocetin induced platelet aggregation curve which strongly suggested von Willebrand's disease type