Abstract

Primary malignant mesenchymomas of the liver are rare malignant tumor of childhood. histologically they are characteracterized by mixture of epithelium-lined cystic structures resembling bile duct, and undifferentiated sarcomatous component. Eosinophilic globules that are PAS positive are seen in or near some of the sarcomatous cells. The present case was a 8-year-old girl with a 15-day-history of a right upper quadrant pain, and palpable mass of one week duration on the right upper abdomen. Under the clinical impression of subcapsular hematoma of the liver, right lobe hepatectomy was done. Grossly the mass, 15×12×11㎝, had nodular surface. On cut section, the tumor was tan to gary gelatinous and rubbery, and was well demarcated from the normal liver, but not encapsulated. It had variously sized cysts, and areas of hemorrhages and necrosis. Microscopic examination revealed multiple cystic spaces similar to bile duct, as well as pleomorphic undifferentiated mesenchymal tissue. Eosinophilic globular bodies were frequently found in the cytoplasm of the tumor cells.